Catalog No.
RHC92201
Species reactivity
Human
Host species
Rabbit
Isotype
IgG
Clonality
Monoclonal
Applications
IF, IHC, WB
Recommended Dilution
| Application |
Dilution |
| IF |
1:50-1:200, IHC: 1:50-1:100, WB: 1:500-1:1000 |
Target
COL6A1, Collagen alpha-1(VI) chain
Concentration
1 mg/ml
Endotoxin level
Please contact with the lab for this information.
Purity
>95% by SDS-PAGE.
Purification
Protein A/G purified from cell culture supernatant.
Accession
P12109
Form
Liquid
Storage buffer
0.01M PBS, pH 7.4, 0.05% BSA, 50% Glycerol, 0.05% Sodium azide.
Stability and Storage
Use a manual defrost freezer and avoid repeated freeze thaw cycles. Store at 4 ℃ for frequent use. Store at -20 ℃ for twelve months from the date of receipt.
Clone ID
R1N58
Note
For research use only.
Morphological classification of nuchal skin in human fetuses with trisomy 21, 18, and 13 at 12-18 weeks and in a trisomy 16 mouse., PMID:9497154
Collagen VI deficiency induces early onset myopathy in the mouse: an animal model for Bethlem myopathy., PMID:9817932
Collagen VI deficiency affects the organization of fibronectin in the extracellular matrix of cultured fibroblasts., PMID:11691587
Dominant and recessive COL6A1 mutations in Ullrich scleroatonic muscular dystrophy., PMID:16130093
The congenital muscular dystrophies: recent advances and molecular insights., PMID:17163796
A refined diagnostic algorithm for Bethlem myopathy., PMID:18378883
Identification and characterization of novel collagen VI non-canonical splicing mutations causing Ullrich congenital muscular dystrophy., PMID:19309692
Expression of the collagen VI α5 and α6 chains in normal human skin and in skin of patients with collagen VI-related myopathies., PMID:20882040
Expression of collagen VI α5 and α6 chains in human muscle and in Duchenne muscular dystrophy-related muscle fibrosis., PMID:22226732
[Clinical and mutation analyses of a Chinese family with Bethlem myopathy]., PMID:23290209
A pilot study comparing protein expression in different segments of the normal colon and rectum and in normal colon versus adenoma in patients with Lynch syndrome., PMID:23604467
Collagen VI regulates satellite cell self-renewal and muscle regeneration., PMID:23743995
Influence of ranibizumab treatment on the extracellular matrix in patients with neovascular age-related macular degeneration., PMID:24866589
Accessibilome of human glioblastoma: collagen-VI-alpha-1 is a new target and a marker of poor outcome., PMID:25325876
Lack of Collagen VI Promotes Wound-Induced Hair Growth., PMID:25989472
RANKL expressed on synovial fibroblasts is primarily responsible for bone erosions during joint inflammation., PMID:26025971
Authentication of collagen VI antibodies., PMID:28755659
Type VI collagen α1 chain polypeptide in non-triple helical form is an alternative gene product of COL6A1., PMID:29659864
Identification of a common epitope in the sequences of COL4A1 and COL6A1 recognized by monoclonal antibody #141., PMID:30321347
The circadian regulator Bmal1 in joint mesenchymal cells regulates both joint development and inflammatory arthritis., PMID:30612576
Localization, fate and interactions of Emilin-1 in human skin., PMID:30843221
Gapmer Antisense Oligonucleotides to Selectively Suppress the Mutant Allele in COL6A Genes in Dominant Ullrich Congenital Muscular Dystrophy., PMID:32865794
Involvement of muscle satellite cell dysfunction in neuromuscular disorders: Expanding the portfolio of satellite cell-opathies., PMID:35302338
The UCMD-Causing COL6A1 (c.930 + 189C > T) Intron Mutation Leads to the Secretion and Aggregation of Single Mutated Collagen VI α1 Chains., PMID:40225172
For research use only. Not for human or drug use.
