Catalog No.
RHP00701
Species reactivity
Human
Host species
Mouse
Isotype
IgG1
Clonality
Monoclonal
Tested applications
IHC: 1:500-1:1000, WB: 1:500-1:1000
Target
Autoimmune enteropathy-related antigen AIE-75, USH1C, Harmonin, Usher syndrome type-1C protein, Protein PDZ-73, Antigen NY-CO-38/NY-CO-37, Renal carcinoma antigen NY-REN-3, AIE75
Concentration
1 mg/ml
Endotoxin level
Please contact with the lab for this information.
Purity
>95% as determined by SDS-PAGE.
Purification
Protein A/G purified from cell culture supernatant.
Accession
Q9Y6N9
Applications
IHC, WB
Form
Liquid
Storage buffer
0.01M PBS, pH 7.4, 0.05% Sodium Azide.
Stability and Storage
Use a manual defrost freezer and avoid repeated freeze-thaw cycles. Store at 4°C short term (1-2 weeks). Store at -20°C 12 months. Store at -80°C long term.
Clone ID
R4C29
Detection of VAR2CSA-Captured Colorectal Cancer Cells from Blood Samples by Real-Time Reverse Transcription PCR., PMID:34884994
Perianal Crohn's Disease is Associated with Distal Colonic Disease, Stricturing Disease Behavior, IBD-Associated Serologies and Genetic Variation in the JAK-STAT Pathway., PMID:26937622
Gastrointestinal immunity against tryptophan hydroxylase-1, aromatic L-amino-acid decarboxylase, AIE-75, villin and Paneth cells in APECED., PMID:25805658
Disease specificity of anti-tryptophan hydroxylase-1 and anti-AIE-75 autoantibodies in APECED and IPEX syndrome., PMID:25463430
Autoantibodies to harmonin and villin are diagnostic markers in children with IPEX syndrome., PMID:24250806
Improved biolistic transfection of hair cells., PMID:23049715
Autoantibodies to villin occur frequently in IPEX, a severe immune dysregulation, syndrome caused by mutation of FOXP3., PMID:21741320
Analysis of subcellular localization of Myo7a, Pcdh15 and Sans in Ush1c knockout mice., PMID:21156003
Harmonin-b, an actin-binding scaffold protein, is involved in the adaptation of mechanoelectrical transduction by sensory hair cells., PMID:19756723
Harmonin in the murine retina and the retinal phenotypes of Ush1c-mutant mice and human USH1C., PMID:19324851
An isoform of GTPase regulator DOCK4 localizes to the stereocilia in the inner ear and binds to harmonin (USH1C)., PMID:16464467
Photoreceptor expression of the Usher syndrome type 1 protein protocadherin 15 (USH1F) and its interaction with the scaffold protein harmonin (USH1C)., PMID:15928608
Differential distribution of harmonin isoforms and their possible role in Usher-1 protein complexes in mammalian photoreceptor cells., PMID:14578428
The Usher syndrome proteins cadherin 23 and harmonin form a complex by means of PDZ-domain interactions., PMID:12407180
Isoforms of the human PDZ-73 protein exhibit differential tissue expression., PMID:10209257
For research use only. Not for human or drug use.
