Catalog No.
RHH03301
Species reactivity
Human
Host species
Mouse
Isotype
IgG2a, kappa
Clonality
Monoclonal
Target
PLEC1, HD1, Hemidesmosomal protein 1, Plectin, Plectin-1, PLTN, PLEC, PCN
Concentration
1 mg/ml
Endotoxin level
Please contact with the lab for this information.
Purity
>95% as determined by SDS-PAGE.
Purification
Protein A/G purified from cell culture supernatant.
Accession
Q15149
Applications
ELISA
Form
Liquid
Storage buffer
0.01M PBS, pH 7.4.
Stability and Storage
Use a manual defrost freezer and avoid repeated freeze-thaw cycles. Store at 4°C short term (1-2 weeks). Store at -20°C 12 months. Store at -80°C long term.
Clone ID
SAA1780
Molecular mimicry-driven autoimmunity in chronic rhinosinusitis with nasal polyps., PMID:39984131
Identification of Pathogenic Pathways for Recurrence of Focal Segmental Glomerulosclerosis after Kidney Transplantation., PMID:39125467
Collagen IV and Podocyte-Related Gene Variants in Patients with Concurrent IgA Nephropathy and Thin Basement Membrane Nephropathy., PMID:36349777
Novel compound heterozygous mutations in the PLEC gene in a neonate with epidermolysis bullosa simplex with pyloric atresia., PMID:35996939
Clinical heterogeneity in epidermolysis bullosa simplex with plectin (PLEC) mutations-A study of six unrelated families from India., PMID:35579050
The Bioactive Peptide SL-13R Expands Human Umbilical Cord Blood Hematopoietic Stem and Progenitor Cells In Vitro., PMID:33915948
Eosinophils are the main cellular targets for oral gene delivery using Lactic acid bacteria., PMID:32197922
Plectin-1 Targeted Dual-modality Nanoparticles for Pancreatic Cancer Imaging., PMID:29574092
Early detection of pancreatic cancer: impact of high-resolution imaging methods and biomarkers., PMID:27769077
Vimentin-mediated regulation of cell motility through modulation of beta4 integrin protein levels in oral tumor derived cells., PMID:26646105
Plectin as a prognostic marker in non-metastatic oral squamous cell carcinoma., PMID:26306491
Plectin-related skin diseases., PMID:25530118
Stabilization of the dystroglycan complex in Cajal bands of myelinating Schwann cells through plectin-mediated anchorage to vimentin filaments., PMID:23836526
Epidermolysis bullosa simplex ogna revisited., PMID:22854623
The RON-receptor regulates pancreatic cancer cell migration through phosphorylation-dependent breakdown of the hemidesmosome., PMID:22275185
Plectin deficiency leads to both muscular dystrophy and pyloric atresia in epidermolysis bullosa simplex., PMID:20665883
Targeted inactivation of a developmentally regulated neural plectin isoform (plectin 1c) in mice leads to reduced motor nerve conduction velocity., PMID:19625254
Plectin 1f scaffolding at the sarcolemma of dystrophic (mdx) muscle fibers through multiple interactions with beta-dystroglycan., PMID:17389230
Biochemical activities of three pairs of Ehrlichia chaffeensis two-component regulatory system proteins involved in inhibition of lysosomal fusion., PMID:16926392
Targeted ablation of plectin isoform 1 uncovers role of cytolinker proteins in leukocyte recruitment., PMID:16344482
Identification of trichoplein, a novel keratin filament-binding protein., PMID:15731013
Epidermolysis bullosa simplex associated with pyloric atresia is a novel clinical subtype caused by mutations in the plectin gene (PLEC1)., PMID:15681471
Plectin., PMID:15646637
Life-long course and molecular characterization of the original Dutch family with epidermolysis bullosa simplex with muscular dystrophy due to a homozygous novel plectin point mutation., PMID:15206692
[Congenital myasthenic syndromes: phenotypic expression and pathophysiological characterisation]., PMID:15034473
Severe mucous membrane involvement in epidermolysis bullosa simplex with muscular dystrophy due to a novel plectin gene mutation., PMID:14963703
Specificity of binding of the plectin actin-binding domain to beta4 integrin., PMID:14517317
Identification of keratinocyte-specific markers using phage display and mass spectrometry., PMID:12644568
Regulation of the association of alpha 6 beta 4 with vimentin intermediate filaments in endothelial cells., PMID:12441134
A patient with immunological features of paraneoplastic pemphigus in the absence of a detectable malignancy., PMID:12430743
The hyaluronan receptor RHAMM/IHABP in astrocytoma cells: expression of a tumor-specific variant and association with microtubules., PMID:12222834
A dynamically localized histidine kinase controls the asymmetric distribution of polar pili proteins., PMID:12198144
Naringin-sensitive phosphorylation of plectin, a cytoskeletal cross-linking protein, in isolated rat hepatocytes., PMID:12095991
Dynamic testicular adhesion junctions are immunologically unique. I. Localization of p120 catenin in rat testis., PMID:11906917
A site-specific plectin mutation causes dominant epidermolysis bullosa simplex Ogna: two identical de novo mutations., PMID:11851880
Caspase 8-mediated cleavage of plectin precedes F-actin breakdown in acinar cells during pancreatitis., PMID:11841995
Localization of plectin and other related proteins along the sarcolemma in smooth muscle cells of rat colon., PMID:11482454
The dento-epithelial junction: cell adhesion by type I hemidesmosomes in the absence of a true basal lamina., PMID:11453242
[Developments on paraneoplasic pemphigus]., PMID:11395661
Plectin, an unusual target antigen in bullous pemphigoid., PMID:11167694
Differences in the distribution of synemin, paranemin, and plectin in skeletal muscles of wild-type and desmin knock-out mice., PMID:10959821
Identification of the cytolinker plectin as a major early in vivo substrate for caspase 8 during CD95- and tumor necrosis factor receptor-mediated apoptosis., PMID:10891503
The 300-kDa intermediate filament-associated protein (IFAP300) is a hamster plectin ortholog., PMID:10873583
A vesicular bullous pemphigoid with an autoantibody against plectin., PMID:10792240
Epidermolysis bullosa: novel and de novo premature termination codon and deletion mutations in the plectin gene predict late-onset muscular dystrophy., PMID:10652002
Differential localization of two histidine kinases controlling bacterial cell differentiation., PMID:10619016
Epidermolysis bullosa simplex associated with muscular dystrophy: phenotype-genotype correlations and review of the literature., PMID:10570379
Expression of plectin and HD1 epitopes in patients with epidermolysis bullosa simplex associated with muscular dystrophy., PMID:10552210
Myopathy, myasthenic syndrome, and epidermolysis bullosa simplex due to plectin deficiency., PMID:10446808