Catalog No.
RHN91901
Species reactivity
Human
Host species
Mouse
Isotype
IgG1
Clonality
Monoclonal
Tested applications
FCM: 1:200-1:400, IF: 1:200-1:1000, WB: 1:500-1:2000
Target
KLHL11, Kelch-like protein 11
Concentration
1 mg/ml
Endotoxin level
Please contact with the lab for this information.
Purity
>95% as determined by SDS-PAGE.
Purification
Protein A/G purified from cell culture supernatant.
Accession
Q9NVR0
Applications
FCM, IF, WB
Form
Liquid
Storage buffer
0.01M PBS, pH 7.4, 0.05% Sodium Azide.
Stability and Storage
Use a manual defrost freezer and avoid repeated freeze-thaw cycles. Store at 4°C short term (1-2 weeks). Store at -20°C 12 months. Store at -80°C long term.
Clone ID
R4A85
The Clinical Trial Landscape in Autoimmune Encephalitis: Challenges and Opportunities., PMID:40146951
Exploring autoantigens in autoimmune limbic encephalitis using phage immunoprecipitation sequencing., PMID:40133514
Upper motor neuron-predominant motor neuron disease: a novel immunotherapy-responsive association of GAD65 autoimmunity., PMID:39998694
Paraneoplastic KLHL11 encephalitis presenting with progressive tinnitus, hearing loss and ataxia., PMID:39978939
High-Throughput Immunoassays for Cavin-4 IgG: A Diagnostic Tool for Immune-Mediated Rippling Muscle Disease., PMID:39957412
Autoimmune encephalitis: recovery, residual symptoms and predictors of long-term sequelae., PMID:39832911
Clinical Manifestations and Treatment Responses in Pediatric Neurofascin 155-IgG4 Autoimmune Nodopathy., PMID:39823553
Unraveling calcium dysregulation and autoimmunity in immune mediated rippling muscle disease., PMID:39819455
MOG antibody-associated disease epidemiology in Olmsted County, USA, and Martinique., PMID:39812824
Frequency, characteristics, and immunological accompaniments of ataxia in anti-NMDAR antibody-associated encephalitis., PMID:39735552
Autoimmune brainstem encephalitis: Clinical associations, outcomes, and proposed diagnostic criteria., PMID:39708293
Case report: The case report of ofatumumab, a fully human anti-CD20 monoclonal antibody, in the treatment of KLHL11 encephalitis., PMID:39575244
Phenotypic and oncological insights in ANNA1 autoimmunity: Age stratification and biomarker analysis., PMID:39556523
Autoimmune Encephalitis and Paraneoplastic Neurologic Syndromes: A Nationwide Study on Epidemiology and Antibody Testing Performance., PMID:39467237
Comprehensive Analysis of Paraneoplastic Neurologic Syndrome and PNS-CARE Diagnostic Criteria in Clinical Practice., PMID:39321395
Teaching Video NeuroImage: Perivascular Tumefactive Neurosarcoidosis of the Basal Ganglia., PMID:39284110
Long-term outcomes in antibody-negative autoimmune encephalitis: a retrospective study., PMID:39278895
Autoimmune Movement Disorders., PMID:39088289
Seizure-Related Falls and Near Falls in LGI1-IgG Autoimmune Encephalitis., PMID:38938695
Clinical and serological insights into paraneoplastic brachial amyotrophic diplegia., PMID:38772930
Magnetic Resonance Imaging Characteristics of LGI1-Antibody and CASPR2-Antibody Encephalitis., PMID:38497971
Pearls & Oy-sters: KLHL11 IgG Paraneoplastic-Associated Hearing Loss and Rhombencephalitis in a Woman With Metastatic Müllerian Tumor., PMID:38484225
Immune Checkpoint Inhibitor-Associated Kelch-Like Protein-11 IgG Brainstem Encephalitis., PMID:38484218
Neurological autoimmunity in patients with non-pulmonary neuroendocrine neoplasms: clinical manifestations and neural autoantibody profiles., PMID:38466015
Overview of Paraneoplastic Autoantibody-Mediated Cognitive Impairment and Behavioral Changes: A Narrative Review., PMID:38322089
Peripheral nervous system manifestations of MOG antibody associated disease., PMID:38234084
Kelch-like Protein 11 (KLHL11) Antibodies in Children With Seizures of Undetermined Cause., PMID:38148071
Kelch-like Protein-11 Encephalitis Associated With Squamous Cell Carcinoma of Unknown Origin: A Case Report., PMID:37982047
Anti-Kelch-like protein 11 antibody encephalitis: a case report and literature review., PMID:37954647
KLHL11 antibody-associated autoimmune encephalomyelitis in a middle-aged female patient: a case report and literature review., PMID:37881832
CDR2 and CDR2L line blot performance in PCA-1/anti-Yo paraneoplastic autoimmunity., PMID:37841252
Identification of SKOR2 IgG as a novel biomarker of paraneoplastic neurologic syndrome., PMID:37795104
Utility of Protein Microarrays for Detection of Classified and Novel Antibodies in Autoimmune Neurologic Disease., PMID:37550073
Stiff person spectrum disorder diagnosis, misdiagnosis, and suggested diagnostic criteria., PMID:37212351
Autoimmune Encephalitis Criteria in Clinical Practice., PMID:37124463
Paraneoplastic Kelch-like protein 11 antibody-associated cerebellar and limbic encephalitis caused by metastatic "burned-out" seminoma - A scar(r)y phenomenon., PMID:36989702
Anti-kelchlike protein 11 antibody-associated encephalitis: Two case reports and review of the literature., PMID:36815561
Paraneoplastic Neurologic Disorders., PMID:36781586
Dual ankyrinG and subpial autoantibodies in a man with well-controlled HIV infection with steroid-responsive meningoencephalitis: A case report., PMID:36756346
Autoimmune Encephalitis Misdiagnosis in Adults., PMID:36441519
Characterization of cardiac bradyarrhythmia associated with LGI1-IgG autoimmune encephalitis., PMID:36304459
Validation of MATCH score: a predictive tool for identification of patients with kelch-like protein-11 autoantibodies., PMID:36150843
Bilateral hearing loss preceding rhomboencephalitis - a hint for Kelch-like 11 syndrome., PMID:36112277
Identification of Caveolae-Associated Protein 4 Autoantibodies as a Biomarker of Immune-Mediated Rippling Muscle Disease in Adults., PMID:35696196
Clinical Reasoning: A Dizzy Architect., PMID:35121670
Characterisation of TRIM46 autoantibody-associated paraneoplastic neurological syndrome., PMID:34921120
Long-term MRI changes in a patient with Kelch-like protein 11-associated paraneoplastic neurological syndrome., PMID:34561925
Eculizumab monotherapy for NMOSD: Data from PREVENT and its open-label extension., PMID:34498507
Paraneoplastic cochleovestibulopathy: clinical presentations, oncological and serological associations., PMID:34285066
Opsoclonus-myoclonus syndrome associated with anti Kelch-like protein-11 antibodies in a young female patient without cancer., PMID:33862421