Catalog No.
RHN71401
Species reactivity
Human
Host species
Rabbit
Isotype
IgG
Clonality
Monoclonal
Tested applications
WB: 1:500-1:1000
Target
Muscleblind-like protein 1, MBNL, EXP, MBNL1, KIAA0428, Triplet-expansion RNA-binding protein
Concentration
1 mg/ml
Endotoxin level
Please contact with the lab for this information.
Purity
>95% by SDS-PAGE.
Purification
Protein A/G purified from cell culture supernatant.
Accession
Q9NR56
Applications
WB
Form
Liquid
Storage buffer
0.01M PBS, pH 7.4, 0.05% BSA, 50% Glycerol, 0.05% Sodium azide.
Stability and Storage
Use a manual defrost freezer and avoid repeated freeze thaw cycles. Store at 4 ℃ for frequent use. Store at -20 ℃ for twelve months from the date of receipt.
Clone ID
R2Q71
Application of Antisense Conjugates for the Treatment of Myotonic Dystrophy Type 1., PMID:36769018
iPSC-derived cardiomyocytes from patients with myotonic dystrophy type 1 have abnormal ion channel functions and slower conduction velocities., PMID:33510259
FISH Protocol for Myotonic Dystrophy Type 1 Cells., PMID:31586350
Quantitative Studies of Muscleblind Proteins and Their Interaction With TCF4 RNA Foci Support Involvement in the Mechanism of Fuchs' Dystrophy., PMID:31560764
Splicing regulators in endothelial cell differentiation., PMID:28661931
RNA interference targeting CUG repeats in a mouse model of myotonic dystrophy., PMID:23183533
Muscle-specific kinase-antibody-positive myasthenia gravis after autologous bone marrow transplantation., PMID:22538309
Expanded CUG repeats Dysregulate RNA splicing by altering the stoichiometry of the muscleblind 1 complex., PMID:21900255
Monoclonal antibodies against Muscleblind-like 3, a protein with punctate nuclear localization., PMID:21529292
Alternative splicing dysregulation secondary to skeletal muscle regeneration., PMID:21400563
A GFP-tagged muscleblind C protein isoform reporter construct., PMID:20855964
RNA/MBNL1-containing foci in myoblast nuclei from patients affected by myotonic dystrophy type 2: an immunocytochemical study., PMID:19864209
Muscleblind-like proteins: similarities and differences in normal and myotonic dystrophy muscle., PMID:19095965
A putative role of ribonuclear inclusions and MBNL1 in the impairment of gallbladder smooth muscle contractility with cholelithiasis in myotonic dystrophy type 1., PMID:18653337
Developmental regulation of muscleblind-like (MBNL) gene expression in the chicken embryo retina., PMID:18095352
Growth-dependent effect of muscleblind knockdown on Caenorhabditis elegans., PMID:18082131
Defective mRNA in myotonic dystrophy accumulates at the periphery of nuclear splicing speckles., PMID:17825047
Protein composition of the intranuclear inclusions of FXTAS., PMID:16246864
For research use only. Not for human or drug use.
