Catalog No.
RHE03801
Species reactivity
Human, Mouse, Rat
Host species
Rabbit
Isotype
IgG
Clonality
Monoclonal
Tested applications
FCM: 1:20-1:100, IF: 1:50-1:200, WB: 1:1000-1:2000
Target
ABC42, Abcd1, ALD, Aldgh, ALDP, AMN, ABCD1
Concentration
1 mg/ml
Endotoxin level
Please contact with the lab for this information.
Purity
>95% by SDS-PAGE.
Purification
Protein A/G purified from cell culture supernatant.
Accession
P33897
Applications
FCM, IF, WB
Form
Liquid
Storage buffer
0.01M PBS, pH 7.4, 0.05% BSA, 50% Glycerol, 0.05% Sodium azide.
Stability and Storage
Use a manual defrost freezer and avoid repeated freeze-thaw cycles.
Store at +4 ℃ short term (1-2 weeks).
Store at -20 ℃ 12 months.
Store at -80 ℃ long term.
Clone ID
R1B54
Secondary failure of lentiviral vector gene therapy in a cerebral adrenoleukodystrophy patient with an ABCD1 whole-gene deletion., PMID:39108094
Phase I clinical trial of intracerebral injection of lentiviral-ABCD1 for the treatment of cerebral adrenoleukodystrophy., PMID:39025777
Structural bioinformatics studies of six human ABC transporters and their AlphaFold2-predicted water-soluble QTY variants., PMID:38577032
Adrenoleukodystrophy in the Differential Diagnosis of Boys Presenting with Primary Adrenal Insufficiency without Adrenal Antibodies., PMID:32394691
Induction of peroxisomal changes in oligodendrocytes treated with 7-ketocholesterol: Attenuation by α-tocopherol., PMID:30031877
Microglial dysfunction as a key pathological change in adrenomyeloneuropathy., PMID:29059709
Role of NH2-terminal hydrophobic motif in the subcellular localization of ATP-binding cassette protein subfamily D: common features in eukaryotic organisms., PMID:25301552
Impaired very long-chain acyl-CoA β-oxidation in human X-linked adrenoleukodystrophy fibroblasts is a direct consequence of ABCD1 transporter dysfunction., PMID:23671276
ABCD2 is a direct target of β-catenin and TCF-4: implications for X-linked adrenoleukodystrophy therapy., PMID:23437103
Intravenous immunoglobulin treatment in a patient with adrenomyeloneuropathy., PMID:23009600
Adrenoleukodystrophy: a forgotten diagnosis in children with primary Addison's disease., PMID:22914231
X-linked adrenomyeloneuropathy due to a novel missense mutation in the ABCD1 start codon presenting as demyelinating neuropathy., PMID:22176151
Expression of aldehyde dehydrogenase and CD133 defines ovarian cancer stem cells., PMID:21480217
The Arabidopsis ALDP protein homologue COMATOSE is instrumental in peroxisomal acetate metabolism., PMID:17581114
Diagnosis of X-linked adrenoleukodystrophy in blood leukocytes., PMID:17524384
Existence of catalase-less peroxisomes in Sf21 insect cells., PMID:12788084
Co-expression of mutated and normal adrenoleukodystrophy protein reduces protein function: implications for gene therapy of X-linked adrenoleukodystrophy., PMID:11063720
Characterization of a novel mutation in exon 10 of the adrenoleukodystrophy gene., PMID:9712540
X-linked adrenoleukodystrophy: improved prenatal diagnosis using both biochemical and immunological methods., PMID:9686376
Two novel missense mutations in the ATP-binding domain of the adrenoleukodystrophy gene: immunoblotting and immunocytological study of two patients., PMID:9212180
Mutational analysis of an X-linked adrenoleukodystrophy (ALD) patient with detectable ALD protein., PMID:8993616
Topology of ATP-binding domain of adrenoleukodystrophy gene product in peroxisomes., PMID:8900413
Altered expression of ALDP in X-linked adrenoleukodystrophy., PMID:7668254
The gene responsible for adrenoleukodystrophy encodes a peroxisomal membrane protein., PMID:8004093
For research use only. Not for human or drug use.
